What is the condition called that involves the progressive obliteration of extra and intrahepatic ducts as well as the gallbladder in early life?

Biliary atresia is a congenital condition characterized by the progressive obliteration of the bile ducts, both extrahepatic and intrahepatic, as well as the gallbladder. This condition leads to a disruption in the flow of bile from the liver to the intestine, causing bile to accumulate in the liver, which can lead to liver damage and cirrhosis if not treated promptly.

The early presentation of biliary atresia usually occurs in infants, often as the child appears jaundiced shortly after birth. A definitive diagnosis typically requires imaging studies and possibly a liver biopsy, but it is crucial to recognize the condition early, as surgical intervention is often needed to restore bile flow and prevent severe complications.

Other conditions mentioned, such as cholelithiasis (gallstones), cholangitis (infection of the bile duct), and pancreatitis (inflammation of the pancreas), are unrelated to the progressive obliteration of the bile ducts seen in biliary atresia, further reinforcing why biliary atresia is the correct choice in this context.